Primary Sjögren’s Syndrome is a diagnosis given when the person has no other autoimmune disease.
This is not exactly true though as I was told I had Primary Sjogren's even though I had an autoimmune thyroid disease. Apparently autoimmune thyroid diseases are so prevalent in people with SS that they have been taken out of the equation.
When Henrik Sjögren, the Swedish ophthalmologist, presented his thesis on Sjögren's in 1933, there was no such thing as Primary and Secondary there was just the name Sjögren's syndrome. He wrote about 19 female patients with lacrimal dysfunction and dryness as keratoconjunctivitis sicca, meaning "inflammation of the cornea and conjunctiva" 13 of whom had arthritis.
The symptoms of Sjögren’s Syndrome vary greatly between individuals and include a dryness of the moist areas of the body, like the mouth, eyes, ears, nose and vagina. Fatigue and depression, plus painful joints, are also associated with the disease.
When organs other than the lacrimal and salivary glands are affected, this is known as “extraglandular involvement.” Usually, this occurs in patients with primary Sjögren’s syndrome (see “Primary Versus Secondary Sjögren’s Syndrome”).
Manifestations of Primary Sjögren’s Syndrome include :
- joint inflammation
- particular forms of autoimmune thyroid, kidney, liver, lung, and skin disease
- changes in nerve function of the upper or lower limbs
- small proportion of patients may progress to a form of lymphoma
Did your specialist define this for you?
RESOURCE: National Institute of Arthritis and Musculoskeletal and Skin Diseases (NIAMS)